Resumo

MORET, Yuli  e  GONZALEZ, José María. Basal Cell Nevi syndrome (Gorlin Goltz): Report of case and review of literature. Acta odontol. venez [online]. 2004, vol.42, n.2, pp.118-121. ISSN 0001-6365.

The Basal Cell Nevi Syndrome (BCNS) is an autosomal dominant condition with highly variable manifestations, the most frequent being carcinoma of nevoid basal cells of the skin, odontogenic keratocysts of the jaw, and other bone abnormalities. Here, we report a case of BCNS. The patient was characterized on the basis of clinical, radiological and anatomical - pathological examination, and a genetic analysis was also performed. We discuss our findings and compare them with those of other authors.

Palavras-chave : Basal Cell Nevi Syndrome; Odontogenic Keratocysts; Diagnosis.