Abstract

BUENO BRANDAO, Cristina et al.  Dental aspects of a patient with moebius syndrome: Case report. Acta odontol. venez [online]. 2008, vol.46, n.3, pp.319-322. ISSN 0001-6365.

Moebius syndrome is characterized by congenital and non-progressive paralysis of the facial and abducent cranial nerves. The principal manifestations of this syndrome are lack of facial expression, convergent bilateral strabismus and hypoplastic members. The oral findings include micrognatia, heterotrophic implantation of the tongue, ankyloglossia, bifid uvula, cleft palate and dental anomalies. The etiology of Moebius syndrome is unknown and some reports relate, as a main cause, the transitory fetal ischemia during the formation of cranial nucleus. The factors that lead to this ischemia are from ambient, physiopathological or genetic disturbs and use of drugs like Misoprostol during the pregnancy. This paper reports the dental treatment of a female patient with Moebius syndrome, emphasizing the peculiarities observed due to the characteristics of this clinical entity.

Keywords : Moebius syndrome; congenital facial diplegia; dental treatmen.