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Gen

versão impressa ISSN 0016-3503versão On-line ISSN 2477-975X

Resumo

GUZMAN, Amador et al. Carcinoma neuroendocrino de papila de vater: Reporte de un caso y revisión de la literatura. Gen [online]. 2007, vol.61, n.4, pp.298-300. ISSN 0016-3503.

Tumors of the papilla are unusual entities. The incidence is less than 5 % of all new digestive tract neoplasms. It may occur in all age groups, but they are more prevalent in people aged 50-70 years, a slight male predominance. Endocrine neoplasms have a less incidence and only 105 cases are reported in the literature. A case of a 53-year-old male with weight loss, abdominal pain, obstructive jaundice is reported. Abdominal ultrasonography showed hepatomegaly, hepatic lesions, biliary sludge, and pancreatic lesion with intra-extra hepatic biliary tract dilatation. He had a successive upper digestive bleeding, pancreaticoduodenectomy was performed. Histological evaluation showed neuroendocrine carcinoma of the ampulla of Vater, Type I (epithelial) Grade III.

Palavras-chave : Papillary tumors; neuroendocrine carcinoma of the ampulla of Vater; Pancreaticoduodenectomy of Whipple.

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